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2-Aminoadipic Acid 3 2-Aminoadipic Semialdehyde Synthase Inhibition 1 22q11 Deletion Syndrome 1 3-Hydroxyacyl CoA Dehydrogenases 1 6-Hydroxy-Pipecolate 1 6-Oxo-Pipecolate 2 6‐oxo‐pipecolic Acid 1 Absorptiometry 1 Access 1 Acetyl-CoA C-Acetyltransferase 1 Acidosis 3 Activities of Daily Living 1 Acyl Coenzyme A 1 Acyl-CoA Dehydrogenase 2 Adolescent 6 Adult 3 Adults 1 Age of Onset 1 AI 1 Aldehyde Dehydrogenase 8 ALDH7A1 5 ALDH7A1 Deficiency 1 Alleles 2 Alpers Syndrome 1 Alpha Aminoadipic Semialdehyde 4 Amino Acid Metabolism 3 Amino Acid Sequence 3 Amino Acid Substitution 1 Amino Acids 1 Amino Acyl-TRNA Synthetases 1 Aminoacyl-TRNA Synthetases 1 Aminoacylation 1 Aminoadipic Semialdehyde 1 Aminomethyltransferase 1 Anemia 1 Animals 3 Anticonvulsants 1 Antiquitin 2 Arginine 2 Arginine Supplementation 2 Asian People 1 Atrophy 1 Autopsy 1 B6 Vitamer 1 Bariatric Surgery 1 Base Sequence 1 Binding Sites 1 Bioethics 1 Biology 1 Biomarkers 3 Bone Density 1 Bone Mineral Density 1 Brain 2 Brain Diseases 4 Brain Magnetic Resonance Imaging 1 CADRe 1 Cardiomyopathies 1 CARS2 1 Cell Line 1 Cell Respiration 1 Cerebral Cortex 1 Cerebrospinal Fluid 1 CGH 1 Child 17 Child Development 1 Child Nutritional Physiological Phenomena 1 Chlorocebus Aethiops 1 Chromatography 1 Chromosomal Instability 1 Chromosome Breakpoints 1 Chromosome Deletion 1 Chromosome Disorders 1 Chromosome Mapping 1 Chromosomes 4 ClinGen 1 Clinical Competence 1 Clinical Reasoning 1 Clinical Trials 1 CNV 1 Cobalamin Metabolism 1 Cognition 3 Cohort Studies 2 Color 1 Colorado 1 Combination 1 Communication 2 Community Engagement 2 Comparative Genomic Hybridization 1 Complex IV 1 Computer Vision 1 Confidentiality 1 Congenital 1 Congenital Bone Marrow Failure Syndromes 1 Consensus 1 Consensus Guidelines 1 Copy Number Variation 1 Corpus Callosum 1 COS Cells 1 Counselors 1 Craniofacial Abnormalities 1 Crispr 2 Cross-Sectional Studies 2 CurePDE 1 Cystinuria 1 Decision Making 1 Deep Learning 1 Delayed Diagnosis 1 Development 1 Developmental Disabilities 1 Dextromethorphan 1 Diagnosis 1 Diet 3 Diet Therapy 2 Dietary Proteins 1 Dietary Supplements 2 Differential 1 Diffusion Magnetic Resonance Imaging 1 Diffusion Restriction 1 Dihydrolipoamide Dehydrogenase 1 Disclosure 4 Disease Mechanism 1 Disease Mechanisms 3 DNA 1 DNA Mutational Analysis 4 Doppler 1 Drug Industry 1 Drug Therapy 1 Dual Energy X-Ray Absorptiometry 1 Dyskinesias 1 Ear 1 Early Diagnosis 1 Educational Status 1 Electron Transport 1 Electron Transport Complex I 1 Electron Transport Complex IV 1 ELSI 1 Energy Metabolism 1 Enoyl-CoA Hydratase 1 Epilepsy 16 Epileptic Encephalopathy 1 Ethics 8 Evolution 1 Excitatory Amino Acid Antagonists 1 Exome 1 Exome Sequencing 1 Exons 1 False Negative Reactions 1 Family 1 Fatal Outcome 4 Female 22 Fluorescence 1 Fun 1 GA1 3 GABA-A 1 GABRA1 1 Gene Expression 2 Gene Expression Regulation 1 Gene Knockdown Techniques 2 Genes 1 Genetic 1 Genetic Association Studies 2 Genetic Counseling 6 Genetic Diseases 2 Genetic Predisposition to Disease 2 Genetic Testing 7 Genetic Variation 1 Genetics 2 Genome Mapping 1 Genome-Wide Association Study 1 Genomic 1 Genomic Disorders 1 Genomic Structural Variation 1 Genomic Testing 1 Genomics 1 Genotype 2 Glutarates 1 Glutaredoxins 1 Glutaric Acidemia Type 1 1 Glutaric Aciduria Type 1 1 Glutaryl-CoA Dehydrogenase 2 Glycine 3 Glycine Decarboxylase Complex 1 Glycine Dehydrogenase (Decarboxylating) 1 Graphs 1 HCU 1 Health Personnel 1 Heart Defects 1 HEK293 Cells 1 Heterozygote 3 Hirschsprung Disease 1 Homocysteine 1 Homocystinuria 1 Homozygote 1 Host Cell Factor C1 1 HSD10 Disease 1 Human 4 Humans 46 Hydrogen Sulfide 1 Hyperammonemia 2 Hyperglycinemia 6 Hyperhomocysteinemia 1 Hypoglycemia 2 IEM 1 In Situ Hybridization 1 Inborn 2 Inborn Errors 7 Inborn Errors of Metabolism 1 Infant 25 Infant Nutrition Disorders 1 Infant Nutritional Physiological Phenomena 1 Informed Consent 5 Intellectual and Developmental Disabilities 1 Intellectual Disability 4 Intelligence Tests 1 International Cooperation 1 Introns 1 Iron-Sulphur Cluster 1 Justice 1 Kidney 1 Kinetics 1 Lactic 3 Language 1 Large Language Models 2 Larva 1 Lecture 2 Leigh Disease 2 Leukodystrophy 1 Leukoencephalopathy 1 Lipid Metabolism 2 Lipoic Acid 1 Liquid 1 Liver 3 Locomotion 1 Long-Chain 2 Longitudinal Studies 1 Lumbar Vertebrae 1 Lysine 9 Lysine Biochemistry 1 Lysine Catabolism 1 Lysine Reduction Therapies 2 Lysine-Restricted 1 Lysine-Restricted Diet 1 Lysine-Restriction 1 Magnetic Resonance Imaging 4 Magnetic Resonance Spectroscopy 1 Male 25 Management 1 Markdown 1 Megaloblastic 1 Mental Disorders 1 Messenger 1 Metabolic 2 Metabolic Epilepies 1 Metabolic Epilepsy 2 Metal Metabolism 1 Methionine 1 Methylmalonic Acid 1 Methylmalonic Acidemia 1 MHBD Disease 1 Microarray 1 Microcephaly 1 Middle Aged 1 Mild 1 Missense 4 Mitochondria 2 Mitochondrial 2 Mitochondrial Diseases 1 Mitochondrial Membrane Transport Proteins 1 Mitochondrial Precursor Protein Import Complex Proteins 1 Mitochondrial Proteins 1 Mitochondrial Translation 1 Molecular 1 Molecular Sequence Data 2 Molybdoferredoxin 1 MONDO 1 Morbid 1 Mosaicism 1 Motor Activity 1 Motor Disorders 1 Mouse Model 1 MRI 1 MRPP2 1 Multienzyme Complexes 1 Muscles 1 Muscular Diseases 1 Mutation 11 Myocardium 1 NADH Dehydrogenase 1 National Institutes of Health 1 Natural History 1 Neonatal Encephalopathy 1 Neonatal Screening 3 Neonatal Seizures 1 Neurodevelopmental Disorders 1 Neurodevelopmental Outcome 1 Neurological Outcome 1 Neuropsychological Tests 1 Newborn 18 Newborn Screening 2 Newsletter 1 NLP 1 Nonketotic 6 Nonketotic Hyperglycinemia 2 Nucleic Acid 1 Nutrition 1 Obesity 1 Oligonucleotide Array Sequence Analysis 1 Organic Acidemia 1 Organic Aciduria 1 Ornithine Carbamoyltransferase Deficiency Disease 1 Orotate Phosphoribosyltransferase 1 Orotic Acid 1 Orotidine-5'-Phosphate Decarboxylase 1 Orphan Drug Production 1 Osteoporosis 1 Oxidation-Reduction 1 Oxidoreductases Acting on Sulfur Group Donors 1 Pair 15 1 Pair 16 2 Pair 22 1 Patient-Reported Outcomes 1 PDE 2 PDE-ALDH7A1 18 PDE‐ALDH7A1 1 Pediatric Ethics 1 Pediatrics 1 Penicillamine 1 Persons With Disabilities 1 Pharmaceuticals 1 Phenotype 6 Phenotypic Outcome 1 Photon 1 Pipecolic Acids 3 Piperideine‐6‐carboxylate 1 PLPBP 1 PNPO 1 Podcast 6 Polymorphism 1 Portal Vein 1 Post-Transcriptional 1 Practice Guidelines as Topic 2 Precision Medicine 1 Predictive Value of Tests 1 Preschool 13 Primary Health Care 1 Primates 1 Principles 1 Prognosis 1 PROMIS 1 Propionic Acidemia 1 Prospective Studies 1 Protein 1 Protein Binding 1 Protein Structure 1 Protein Subunits 1 Proteins 1 Proteomics 1 Public-Private Sector Partnerships 1 Purine-Pyrimidine Metabolism 1 Pyridoxine 9 Pyridoxine-Dependent Epilepsy 6 Pyridoxine-Responsive Seizures 1 Pyridoxine‐dependent Epilepsy 2 Pyrimidines 1 Pyruvate Dehydrogenase (Lipoamide) 1 Pyruvate Dehydrogenase Complex Deficiency Disease 1 Quinone Reductases 1 Rare Disease Studies 3 Rare Diseases 2 Receptors 1 Recommended Dietary Allowances 1 Refractory Seizures 1 Repetitive Sequences 1 Repressor Proteins 1 Reserach 1 Restricted Diffusion 1 Restrictive Cardiomyopathy 1 Results Disclosure 2 Retrospective Studies 5 Return of Results 1 Risk Factors 1 RNA 2 RNA Processing 1 RNase P 1 Rubric 1 Secondary 1 Segmental Duplications 1 Seizures 4 Sequence Alignment 1 Sequence Deletion 1 Service Delivery 1 Severe Short Stature 1 Severity of Illness Index 1 Sibling Study 1 Siblings 1 Single Nucleotide 1 Single Nucleotide Polymorphism 1 Small Interfering 1 SNP 1 Sodium Benzoate 1 Source Themes 1 Spectrum Analysis 1 Structural Variation 1 Students 1 Sudden Infant Death 2 Sulfide:quinone Oxidoreductase 1 Sulfurtransferases 1 Surveys and Questionnaires 1 Systems Biology 1 Tandem Mass Spectrometry 1 Therapeutic Advances 3 Therapeutics 1 Therapy 1 Time-to-Treatment 1 Tomography 1 Transcription 1 Transfer 1 Treatment 2 Tryptophan 1 Ultrasonography 1 United States 3 Urea Cycle Disorders 3 Uridine 1 Urinary Calculi 1 Urinary Tract 1 Vascular Malformations 1 Vitamin B 12 1 Vitamin B 12 Deficiency 1 Vitamin B Complex 2 Vitamin B6 2 Weight Loss 1 White Matter 1 Williams Syndrome 1 X 1 X-Linked 2 X-Linked Intellectual Disability 1 X-Ray Computed 1 Young Adult 2 Zebrafish 1